Lege Artis Medicinae

[Intimal sarcoma of the pulmonary artery]

NAGY Pál, TOMCSÁNYI István, MAGYAR Éva

APRIL 01, 2009

Lege Artis Medicinae - 2009;19(03)

[INTRODUCTION - Malignant tumours arising from the wall of the pulmonary artery or the aorta are very rare. Two types are known, leiomyosarcoma and intimal sarcoma. Intimal sarcoma is usually associated with a thrombus that may close the lumen, which complication being important in case of pulmonary artery tumours. Such tumours can be diagnosed by magnetic resonance imaging (MRI). CASE REPORT - A 42-year-old woman was hospitalized with an anamnesis of three months of subfebrility/fever, dyspnea and hemoptysis. Right-sided pulmonary thromboembolism and exudative pleuritis were diagnosed. MRI findings suggested a tumour of the right pulmonary trunk. She underwent surgery with extracorporeal circulation; and a compact mass with a connected thrombus filling the right pulmonary trunk and its hilar branches were removed by thromboendarterectomy. Histology revealed intimal sarcoma of the pulmonary artery. The patient died of this tumour’s progression four years later. CONCLUSION - In case of pulmonary thromboembolism the possibility of intimal sarcoma has to be considered. Vascular tumours can be proven or excluded by MRI.]

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