Journal of Nursing Theory and Practice

[Healthcare and social aspects of nursing in relation to the rare Pompe disease]

TÓTH Mónika1, VÁRDI Katalin Borbála1

AUGUST 28, 2014

Journal of Nursing Theory and Practice - 2014;27(04)

[Aim of the study: Pompe disease is a rare mitochondrial disease, which is treated with enzyme replacement therapy. The authors examined the lifestyles of patients diagnosed with Pompe disease, and their knowledge regarding the illness. They compared this with the results of the regular checkups performed during the care process, in order to assess the patients’ compliance. Sample and methods: The research was conducted among patients suffering from Pompe disease, treated at the Rehabilitation Department of the Törökbálint Institute of Pulmonary Medicine (N=14). The survey of the patients’ knowledge took place in the form of personal interviews. The findings related to the regular enzyme replacement therapy were recorded and collated in the course of interviews conducted by telephone with the nurses of the centres administering the treatment. The data was processed using Microsoft Excel software. Results: In 2012 in Hungary the number of patients diagnosed with Pompe disease was 14 (12 adults, 2 children). The time elapsed from emergence of the first symptoms to the precise diagnosis in the case of all known patients (except in the case of one screened child) was an average of 13.4 years. Ten of the patients were receiving enzyme replacement therapy. The survey revealed that the conditions of the patients receiving the enzyme replacement therapy did not deteriorate. In the case of the female child, the decrease in CK levels was accompanied by growth and movement consistent with her age, and an improvement in vocalisation. Conclusions: For patients diagnosed with the once fatal Pompe disease, enzyme replacement therapy now offers the opportunity of a full life; and complementary treatments not only boost the effectiveness of the enzyme replacement, but also improve the patients’ subjective quality of life.]


  1. Törökbálinti Tüdőgyógyintézet Rehabilitációs Osztály



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Journal of Nursing Theory and Practice

[Aggression management programme for healthcare workers]


[Aim of the study: Introducing a programme for aggression prevention and assessing the experiences of its first session in Budapest. Sample and methods: The study was conducted with the involvement of 30 healthcare workers, using a self-administrative questionnaire and a focus group session. The self-administrative questionnaires were used to evaluate the quality of the programme, while the aim of the focus group was to reveal its further details. Results: The training was met by positive responses both in connection with the material and the preparedness of the instructors. During the focus group, numerous sensitive points came to light about the programme, and further suggestions were given this way helping the improvement. Conclusions: The objective and subjective results of the study both support the need for a training that helps prevent aggression. However, further changes are needed in order to increase its effectiveness. ]

Journal of Nursing Theory and Practice

[Examination of effects of the nurses shiftworks with application of Standard Shiftwork Index - pilot study]

FUSZ Katalin, KOVÁCS KALIC Károly, KÍVÉS Zsuzsanna, MÜLLER Ágnes, OLÁH András

[Aim of the study: Several physiological processes are disturbed in shift workers. The authors’s aim was to complete a pilot study as part of the validation process of Standard Shiftwork Index (SSI) and to examine the effects of shiftwork on the quality of sleeping and on psychical and somatic status. Sample and methods: The survey was implemented at the hospitals of the University of Szeged in 2011, with the participation of not randomly selected nurses working in shiftwork, night- or dayshifts (N=211). SSI was complemented with further respective questions. Results: Those working in dayshift suffer less from sleep disorders than nurses working in nightshift or shiftwork (p=0,002, p=0,005), and have better health status (p=0,001, p=0,003), furthermore feel themselves less tired (p=0,011, p=0,039). The nightshift workers had gastrointestinal complaints more frequently (p=0,044, p=0,006), as well as nurses working in nightshift suffer from more chronic diseases than dayshift workers (p=0,004) and shift workers (p=0,003). In case of shift workers the weekly amount of cigarettes having smoked (p=0,008) and the consumption of caffeinated refresher beverages (p<0,001) were significantly increased since the beginning of their shiftwork. Conclusion: Health status of nurses working in nightshifts and shiftwork are more relapsed, their health attitude is worse than in case of dayshift workers. As the continuation of this examination the authors try to find out which variations of shiftwork can be considered less exhausting.]

Journal of Nursing Theory and Practice

[Investigation of graduate students’ health behavior in high school of the small town]


[Aim of the study: To investigate graduate students’ addictions, their attitude towards healthy living and to find connection between the above and their parents’ and teachers’ lifestyle. Sample and methods: Investigating graduate students’ (n=100) and their teachers’ (n=29) lifestyles in a high school of a small town in Békés County. The results were analyzed by using SPSS programme (Cross tabulation analysis, Chi-Square Test). Results: While the students’ and their parents’ addictions are worse than the Nation’s average, the teachers’ tends to be better. 79 % of the parents and 54 % of the students does not do any sports on a daily basis. The parents and teachers can’t improve the students’ lifestyle efficiently. Students with good academic grades seem to lead healthier life. 60 % of the students with C, D grades (worse grades) smoke, while it’s 28 % of those with A and B (better grades). Conclusions: For efficient health education we need dedicated professionals who are able to involve parents to reach the best result. It’s a joint task to show the youngsters the way leading to a healthy life, as well as to give them the ability to be responsible in their choices.]

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Journal of Nursing Theory and Practice

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[Aim of the research: To assess the blood donation-related knowledge of paramedical professionals working in the fields of nursing and care-giving, emergency care, surgical care and obstetric care in Hungary. Sample and method: The anonymous, self-completion questionnaire used in the survey was based on the „Eurobarometer 41.0 (1995): Europeans and Blood” survey, which the authors supplemented with their own questions. The authors conducted a web-based survey. The survey took place between 15 July and 15 September 2012, among paramedical professionals in four different professional groups, using a convenience sampling method. The authors analysed the collected data with IBM SPSS Statistics 20 software and the Kingsoft Office Spreadsheet (2012) program, using a descriptive statistical method and chi square test. Results: The survey took place with the participation of 312 paramedical professionals. Based on the results of the survey it was established that all the professional groups displayed gaps in their knowledge regarding blood donation. 86.19% of respondents have a correct understanding of blood donation. No significant differences can be observed between the levels of knowledge in the individual professional groups. Conclusions: The results display some significant and some non-significant correlations, as well as stochastic relationships relating to the distribution within the submanifolds. In the interest of eliminating the gaps in knowledge that were revealed in respect of the individual issues, the authors highlight the need for further training of paramedical professionals regarding blood donation.]

Journal of Nursing Theory and Practice

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