Lege Artis Medicinae

[INTRAVASCULAR LEIOMYOMATOSIS PRESENTING AS A RIGHT ATRIAL MASS]

MAGYAR Éva, SALAMON Ferenc, TOMCSÁNYI István

OCTOBER 21, 2007

Lege Artis Medicinae - 2007;17(10)

[INTRODUCTION - Intravenous leiomyoma is a peculiar, rare tumour that originates from the myomatous uterus, grows into the lumina of veins and, through the inferior vena cava, may extend to the right heart cavity. The intracardial tumour causes severe cardiovascular symptoms and may be fatal. CASE REPORT - The symptoms of the 45-yearold woman consisted of chest discomfort, dizziness, and short periods of unconsciousness, which occurred during vacuum-cleaning when she bent forward. Imaging showed a growth that filled the lumen of the vena cava and extended to the right atrium, swinging between the atrium and ventricle. The patient underwent surgery with cardiopulmonary bypass and the intracardial tumour was removed together with its extensions filling the veins. The histological examination verified intravenous leiomyomatosis. Although the patient refused the recommended hysterectomy, she is well after six years the operation. CONCLUSION - In cases of unspecific cardiac symptoms, the possibility of intravenous leiomyomatosis should be considered. The diagnosis can be set up by echocardiography, MR or CT scan. If the diagnosis is confirmed, the tumour should be surgically removed.]

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Clinical Neuroscience

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