Lege Artis Medicinae

[Idiopathic arterial calcification of infancy]

SZABÓ Zsuzsanna1

JULY 31, 1991

Lege Artis Medicinae - 1991;1(13)

[Idiopathic arterial calcification of infancy is a rare disease of undetermined etiology characterized by deposition of calcific material along the internal elastic membrane of arteries and accompanied by simultaneous proliferation of the fibrous tissue of the intima resulting in luminal narrowing. The history of an one month old infant has been reported. The clinical signs were characterized by heart failure and hepatic injury caused by idiopathic arterial calcification. In connection with the author's own case literature data on the etiology and mechanism of calcification and the clinical and morphological features of the disease have been reviewed. This case is distinguished from others by the fact that the disease was combined with hepatic injury. ]

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  1. adjunktus Fővárosi Szent László Kórház Pathológiai Osztály Budapest

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