Clinical Neuroscience

Acute motor and sensory axonal neuropathy associated with Sjögren’s syndrome

ETHEMOGLU Ozlem1, KOCATÜRK Özcan1, TARINI Zeynep Emine2

SEPTEMBER 30, 2018

Clinical Neuroscience - 2018;71(09-10)

DOI: https://doi.org/10.18071/isz.71.0352

Sjögren’s syndrome (SS) is an autoimmune disease with mononuclear cell infiltration and destruction of the lacrimal gland and salivary glands, which cause dryness of the eyes and mouth. The most common neurological condition seen in SS is peripheral neuropathy. Initial manifestation of SS as an acute fulminant peripheral neuropathy is extremely rare. We report a 42-year-old patient presenting with acute motor sensory-axonal neuropathy in the presence of SS. She showed partial response to intravenous immunoglobulin but favourable clinical improvement was seen after initiation of corticosteroid treatment.

AFFILIATIONS

  1. Harran University School of Medicine, Department of Neurology, Şanlıurfa, Turkey
  2. Şanlıurfa Mehmet Akif İnan Education and Research Hospital, Department of Pathology, Şanlıurfa, Turkey

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