Lege Artis Medicinae

[Non-immune hydrops caused by double-chambered right ventricle of the heart]

HAJDÚ Júlia1, SZILLER István1, MACHAY Tamás1, SZABÓ István1, PAPP Zoltán1, MARTON Tamás2, SZATMÁRI András3

APRIL 27, 1994

Lege Artis Medicinae - 1994;4(04)

[The isolated double chambered right ventricle is a rare congenital cardiac malformation. No such case diagnosed in utero has been published. Our case was associated with hydrops syndrome. This malformation has not been published as a cause of non-immune hydrops. At the 29th week of gestation, a severe form of isolated double-chambered right ventricle was found in a fetus. The diagnosis was based on echocardiographic examination (ATL, Ult ramark 9, M-mode, 2 dimension Doppler, color-coded Doppler). The malformation caused severe hydrops. The authors had differential diagnostic problems because of the rarity of this case. The most common causes of non-immun hydrops fetalis (40% of the cases) are cardiac abnormalities. Modern, high resolution ultrasonic equipment has provided the possibility of detecting these malformations. The fetal prognosis in such cases is poor. ]

AFFILIATIONS

  1. Semmelweis Orvostudományi Egyetem I. sz. Szülészeti és Nőgyógyászati Klinika
  2. Semmelweis Orvostudományi Egyetem I. sz. Patológiai Intézet
  3. Országos Kardiológiai Intézet Budapest

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