Hungarian Radiology

[Hungarians on the ECR - ECR 2005 meets Hungary]


DECEMBER 20, 2004

Hungarian Radiology - 2004;78(06)



Further articles in this publication

Hungarian Radiology

[Digital radiology in Europe - radiology in digital Europe]

BARTA H. Miklós, FORRAI Gábor, PALKÓ András

Hungarian Radiology

[Melorheostosis Uncommon appearances]


[INTRODUCTION - Melorheostosis is a rare but well publicised disease. About 320 cases were reported up to 1994. The incidence is estimated 0.9 cases per million. CASE REPORT - We report a 40 year-old man diagnosed with severe melorheostosis and unusual radiographic appearances. No dripping candle wax cortical thickening was present. All the long bones of the upper extremities showed extensive periosteal and endosteal hyperostosis with extension of the changes into the hands and shoulder girdle. Osteosclerosis was present at both sides of the right sacro-iliac joint. There was also hypoplasia of the scapulae, distal ulnae, carpal bones and the left thumb. Distinctive features of the clinical history were that the disease was of prenatal origin. The lower extremities were normal and in spite of extensive bone and soft tissue changes in the upper extremities this patient never experienced pain - a prominent feature of adult melorheostosis. CONCLUSION - Melorheostosis is a rare disorder, diagnosis of which can be made from clinical presentation and radiographs. In case of atypical melorheostosis, the lower extremities may be found to be normal on radiographs. The presentation may be painless.]

Hungarian Radiology

[Meeting of the Hungarian College of Radiologists]

PALKÓ András, FORRAI Gábor

Hungarian Radiology

[Loránd Fráter - A president without position; Professor Eberhard Willich is 85 years old; My memories on Hungarians]

LOMBAY Béla,Schläffer Erzsébet, EBERHARD Willich

Hungarian Radiology

[The “other” Röntgen - Julius the composer]


All articles in the issue

Related contents

Clinical Neuroscience

[Advanced Parkinson’s disease characteristics in clinical practice: Results from the OBSERVE-PD study and sub-analysis of the Hungarian data]

TAKÁTS Annamária, ASCHERMANN Zsuzsanna, VÉCSEI László, KLIVÉNYI Péter, DÉZSI Lívia, ZÁDORI Dénes, VALIKOVICS Attila, VARANNAI Lajos, ONUK Koray, KINCZEL Beatrix, KOVÁCS Norbert

[The majority of patients with advanced Parkinson’s disease are treated at specialized movement disorder centers. Currently, there is no clear consensus on how to define the stages of Parkinson’s disease; the proportion of Parkinson’s patients with advanced Parkinson’s disease, the referral process, and the clinical features used to characterize advanced Parkinson’s disease are not well delineated. The primary objective of this observational study was to evaluate the proportion of Parkinson’s patients identified as advanced patients according to physician’s judgment in all participating movement disorder centers across the study. Here we evaluate the Hungarian subset of the participating patients. The study was conducted in a cross-sectional, non-interventional, multi-country, multi-center format in 18 countries. Data were collected during a single patient visit. Current Parkinson’s disease status was assessed with Unified Parkinson’s Disease Rating Scale (UPDRS) parts II, III, IV, and V (modified Hoehn and Yahr staging). Non-motor symptoms were assessed using the PD Non-motor Symptoms Scale (NMSS); quality of life was assessed with the PD 8-item Quality-of-Life Questionnaire (PDQ-8). Parkinson’s disease was classified as advanced versus non-advanced based on physician assessment and on questions developed by the Delphi method. Overall, 2627 patients with Parkinson’s disease from 126 sites were documented. In Hungary, 100 patients with Parkinson’s disease were documented in four movement disorder centers, and, according to the physician assessment, 50% of these patients had advanced Parkinson’s disease. Their mean scores showed significantly higher impairment in those with, versus without advanced Parkinson’s disease: UPDRS II (14.1 vs. 9.2), UPDRS IV Q32 (1.1 vs. 0.0) and Q39 (1.1 vs. 0.5), UPDRS V (2.8 vs. 2.0) and PDQ-8 (29.1 vs. 18.9). Physicians in Hungarian movement disorder centers assessed that half of the Parkinson’s patients had advanced disease, with worse motor and non-motor symptom severity and worse QoL than those without advanced Parkinson’s disease. Despite being classified as eligible for invasive/device-aided treatment, that treatment had not been initiated in 25% of these patients.]

Hungarian Radiology

[The quality control of radiological equipments in Hungary]

PELLET Sándor, PORUBSZKY Tamás, BALLAY László, GICZI Ferenc, MOTOC Anna Mária, VÁRADI Csaba, TURÁK Olivér, GÁSPÁRDY Géza

Clinical Neuroscience


SISKA Éva, NEUWIRTH Magdolna, REBECCA Gooding, MOLNÁR Mária Judit

[The congenital cataracts facial dysmorphism neuropathy (CCFDN) syndrome (OMIM 604168) is a recently described autosomal recessive developmental disorder. It is almost completely restricted to an endogamous group of the European Vlax Roma population, called the Rudari. The CCFDN syndrome is a complex phenotype involving multiple systems, characterized by facial dysmorphism, congenital cataracts, microcorneae, delayed early motor and intellectual development, hypogonadotrop hypogonadism, hypomyelination of the peripheral nervous system, and serious complications related to general anaesthesia. This disorder is caused by a homozygous mutation of the carboxy-terminal domain phosphatase 1 (CTDP1) gene, localized to the 18q23 region. Authors present one genetically identified case in a large Roma family. The case documents that the CCFDN mutation is present also in the Hungarian Roma population. Underlie of antropomorphological data the authors presume that the CCFDN mutation reached Hungary as a result of emigration of Vlax Gypsies in the 18th century. The paper calls attention to the fact that molecular genetic diagnostics can replace invasive methods and makes possible the identification of heterozygotes without clinical symptoms. The introduction of the genetic screening enables us to perform genetic counselling and prevention in this high-risk population.]

Journal of Nursing Theory and Practice

[Advanced, evidence-based care - The care of the mechanically ventillated patient]

FULLÉR Noémi, OLÁH András

[The care of the mechanically ventillated patient is a complex nursing duty what requires comprehensive knowledges from the professionals. The appearance of the nosocomial conditions, costs of the care and days of the care can be decreased by the proper evidence based nursing practice. Many research papers and guidelines were developed at the international literature regarding the mechanically ventillated patients but the well-founded books or studies are missing in Hungary. With this paper the aim is to emphasize the importance of the evidence based nursing practice part of the critically ill patients what is necesary for the eligible care and should be a part of a well-trained health care professional’s knowledge. ]

Journal of Nursing Theory and Practice

[Application of external circulatory assist device in cases of cardiac failure]

TAMÁS Csilla, BARATI Zoltán

[The Heart and Vascular Centre of Semmelweis University was the first institution in Hungary to routinely apply external mechanical circulatory support (Extracorporal Membrane Oxigenation, Ventricular Assist Device) as a new alternative to treat cardiogenic shock cases. The objective of our study was to assess how frequently certain therapeutic methods were applied, and to evaluate the demographic characteristics, the case historic and the mortality data of the patients treated, as well as to demonstrate the incidence rate of the most frequent complications. Our study was based on the data of patients suffering cardiogenic shocks treated with external circulatory assist devices between 1. June, 2012 and 31. January, 2016. The study has been carried out analytically and retrospectively after data collection from written and electronic patient documentation. Data analysis has been executed by SPSS software. The results revealed uneven gender distribution, over 60% of incidence in case of four examined complications, and an elevated mortality rate of patients over 60 years old. We found that there is a higher risk for complications if mechanical circulatory support is applied, and we made a suggestion to reconsider the application of this support for patients over certain ages. The study demonstrated that our results match the statistical data found in international medical literature. ]